Titlebook: Disorders of Porphyrin Metabolism; Michael R. Moore,Kenneth E. L. McColl,Abraham Gold Book 1987 Springer Science+Business Media New York 1

Osteopenia

書目名稱Disorders of Porphyrin Metabolism影響因子(影響力)




書目名稱Disorders of Porphyrin Metabolism影響因子(影響力)學科排名




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書目名稱Disorders of Porphyrin Metabolism網(wǎng)絡公開度學科排名




書目名稱Disorders of Porphyrin Metabolism被引頻次




書目名稱Disorders of Porphyrin Metabolism被引頻次學科排名




書目名稱Disorders of Porphyrin Metabolism年度引用




書目名稱Disorders of Porphyrin Metabolism年度引用學科排名




書目名稱Disorders of Porphyrin Metabolism讀者反饋




書目名稱Disorders of Porphyrin Metabolism讀者反饋學科排名

INTER

Porphyrins and Enzymes of the Heme Biosynthetic Pathway,idges (Fig. 7). This is a rigid planar structure onto which eight side chains can be attached at positions 1 to 8 in the Fischer nomenclature. The type of side chain determines the physical characteristics of the porphyrin. The four pyrrole rings are designated A, B, C, and D and the four methine br

Guileless

alcoholism

Drugs, Chemicals, and Porphyria,h century. This produced the first example of acute porphyria (Stokvis, 1889) and was followed by a number of similar cases. Since that time, a number of commonly used drugs have been linked with the development of acute attacks of these diseases. Workers have used the ability of certain compounds t

為現(xiàn)場

Incumbent

Cutaneous Hepatic Porphyria,ks of neurovisceral dysfunction. The basic biochemical defect is reduced activity of the enzyme uroporphyrinogen decarboxylase (URO.D) in the liver, which results in overproduction and increased excretion of uroporphyrin and other polycarboxylated porphyrins. CHP differs from the other porphyrias in

Incumbent

Erythropoietic Protoporphyria,arly identified by Magnus .. (1961) and Langh?f .. (1961), although there had been earlier reports (Kosenow and Treibs, 1953). At this stage, it was named erythropoietic protoporphyria (EPP), but it became clear from the investigations of Gray .. (1964) and Barnes .. (1968) and from the studies of m

驚呼

Congenital Porphyria, of photosensitivity in early life. There is overproduction of porphyries of the series 1 variety. These accumulate in the normoblasts of the bone marrow and are excreted in excess in the urine and feces. Porphyries are also deposited in the bones and teeth, resulting in a pink-brown discoloration.

Excitotoxin

Porphyrins in Diseases Other than the Porphyrias,ias. Studies of porphyrin metabolism in these conditions provide a useful insight into the underlying disease process as well as being of clinical value in both diagnosing and assessing the severity of the disorder. The abnormal porphyrin metabolism identified in tumor cells has been employed as an

Substitution