標題: Titlebook: Retinal Degenerative Diseases and Experimental Therapy; Joe G. Hollyfield,Robert E. Anderson,Matthew M. La Book 1999 Springer Science+Busi [打印本頁] 作者: informed 時間: 2025-3-21 18:20
書目名稱Retinal Degenerative Diseases and Experimental Therapy影響因子(影響力)
書目名稱Retinal Degenerative Diseases and Experimental Therapy影響因子(影響力)學科排名
書目名稱Retinal Degenerative Diseases and Experimental Therapy網(wǎng)絡公開度
書目名稱Retinal Degenerative Diseases and Experimental Therapy網(wǎng)絡公開度學科排名
書目名稱Retinal Degenerative Diseases and Experimental Therapy被引頻次
書目名稱Retinal Degenerative Diseases and Experimental Therapy被引頻次學科排名
書目名稱Retinal Degenerative Diseases and Experimental Therapy年度引用
書目名稱Retinal Degenerative Diseases and Experimental Therapy年度引用學科排名
書目名稱Retinal Degenerative Diseases and Experimental Therapy讀者反饋
書目名稱Retinal Degenerative Diseases and Experimental Therapy讀者反饋學科排名
作者: constitutional 時間: 2025-3-21 21:50 作者: 過于光澤 時間: 2025-3-22 01:03
Uwe Wolfrum,Angelika Schmittced. With climate change displaced people (CDP) resorting to this as their last adaptation option, the demand for protection regimes grows. Examined here are the macro and macro-macro-UNFCCC (United Nations Framework Convention on Climate Change) laws, policy measures and other norms, particularly t作者: cyanosis 時間: 2025-3-22 06:40 作者: voluble 時間: 2025-3-22 10:59 作者: 出血 時間: 2025-3-22 13:24
T. Michael Redmondn und Gerechtigkeit in der Welt “. Nach fünfunddrei?ig Jahren sieht die Bilanz gemischt aus. Die Hoffnung, dass Kirche und Gesellschaft die Dimension der Entwicklungsaufg?be als ? internationale soziale Frage “ erkennen und dementsprechend die Priorit?ten in der Au?en-, Sicherheits- und Wirtschaftsp作者: 膝蓋 時間: 2025-3-22 19:24
Breandán N. Kennedy,John C. Saari,John W. Crabbn und Gerechtigkeit in der Welt “. Nach fünfunddrei?ig Jahren sieht die Bilanz gemischt aus. Die Hoffnung, dass Kirche und Gesellschaft die Dimension der Entwicklungsaufg?be als ? internationale soziale Frage “ erkennen und dementsprechend die Priorit?ten in der Au?en-, Sicherheits- und Wirtschaftsp作者: 過份艷麗 時間: 2025-3-23 00:41
Hans-Jürgen Fülle,Rima Khankann und Gerechtigkeit in der Welt “. Nach fünfunddrei?ig Jahren sieht die Bilanz gemischt aus. Die Hoffnung, dass Kirche und Gesellschaft die Dimension der Entwicklungsaufg?be als ? internationale soziale Frage “ erkennen und dementsprechend die Priorit?ten in der Au?en-, Sicherheits- und Wirtschaftsp作者: Grasping 時間: 2025-3-23 04:38
David G. Birch,Ruey-Bing Yang,Susan W. Robinson,David L. Garbersn und Gerechtigkeit in der Welt “. Nach fünfunddrei?ig Jahren sieht die Bilanz gemischt aus. Die Hoffnung, dass Kirche und Gesellschaft die Dimension der Entwicklungsaufg?be als ? internationale soziale Frage “ erkennen und dementsprechend die Priorit?ten in der Au?en-, Sicherheits- und Wirtschaftsp作者: cipher 時間: 2025-3-23 07:23
Susan L. Semple-Rowlandn und Gerechtigkeit in der Welt “. Nach fünfunddrei?ig Jahren sieht die Bilanz gemischt aus. Die Hoffnung, dass Kirche und Gesellschaft die Dimension der Entwicklungsaufg?be als ? internationale soziale Frage “ erkennen und dementsprechend die Priorit?ten in der Au?en-, Sicherheits- und Wirtschaftsp作者: 名字的誤用 時間: 2025-3-23 13:13
Matthias C. Grieshaber,Eugen Boltshauser,Günter Niemeyerzugleich diejenigen Themen der Analysis, Differentialgeometrie und der Mathematischen Physik zu behandeln, in denen Formen besonders wichtig sind. Es ent- stand nach zahlreichen Vorlesungen, welche der zweite Autor seit Beginn der 80er Jahre an der Humboldt-Universit?t zu Berlin über Analysis für St作者: 背景 時間: 2025-3-23 13:57 作者: 恩惠 時間: 2025-3-23 18:50 作者: certain 時間: 2025-3-24 00:20
Ching-Hwa Sung,Jen-Zen Chuangt von Antibiotika in Bakterien genannt. Die intrazellul?re Konzentration eines Antibiotikums bestimmt dessen Wirksamkeit. Die meisten Antibiotika erreichen ihren Zielort in der Zelle durch Diffusion, was dazu führt, da? intrazellul?r die gleiche Konzentration wie extrazellul?r erreicht wird. Nur dan作者: 燦爛 時間: 2025-3-24 02:23 作者: Provenance 時間: 2025-3-24 10:06 作者: 微枝末節(jié) 時間: 2025-3-24 11:04 作者: Vo2-Max 時間: 2025-3-24 16:53 作者: CT-angiography 時間: 2025-3-24 19:58
mRNA Analysis of Oguchi Patients with the Frequent 1147delA Mutation in the Arrestin Genee level of mRNA in all of three patients with Oguchi disease. mRNA from Oguchi patients did not have the same 1147delA mutation as was seen in the arrestin gene but had the normal sequence. The result indicated the possibility of RNA editing in blood cells in our patients.作者: 發(fā)誓放棄 時間: 2025-3-25 01:27 作者: LAPSE 時間: 2025-3-25 04:48
Guanylyl Cyclase Genes and Their Role in Retinal Degenerationts. We demonstrate that this mutation markedly decreases enzyme activity when expressed .. Function and possible linkage to eye disease of an X-chromosomal gene encoding a second retinal isoform, ., are less clear. We determined the genomic structure of . as a prerequisite for future mutation screening studies.作者: erythema 時間: 2025-3-25 11:02
Guanylyl Cyclase Gene is the Disease Locus in the , Chickenfants. With the identity of the . gene in hand, it seems appropriate to review the nearly two decades of research that has been conducted on this model, research that has provided a firm foundation for our current efforts to restore sight in these animals using somatic gene therapy.作者: burnish 時間: 2025-3-25 15:42 作者: lattice 時間: 2025-3-25 17:28 作者: 連累 時間: 2025-3-25 22:20
Blindness in Usher Syndrome 1Br the trafficking of phototransductive membrane during various stages of its turnover. Our studies of molecular motors in photoreceptor cells and the RPE are aimed at understanding mechanisms involved in phototransductive membrane turnover and the cellular basis of some forms of retinal degeneration作者: Ebct207 時間: 2025-3-26 00:20 作者: Foreknowledge 時間: 2025-3-26 06:07
The ,-Deficient Mouse as a Model for ,-Associated Leber’s Congenital Amaurosis and Related Disorderstations in the human . gene have been associated with Leber’s congenital amaurosis, a disorder characterized by blindness at birth, and autosomal recessive childhood-onset severe retinal dystrophies. We have developed an .-deficient mouse and have described its phenotype. The .-deficient mouse pheno作者: 兇兆 時間: 2025-3-26 12:29
CRALBP and Inherited Retinal Degenerationntosa (arRP). We show here liquid chromatography electrospray mass spectrometric results from recombinant mutant CRALBP that were instrumental in establishing that the arRP modification was responsible for a loss of protein function. In addition, we present progress in the development of CRALBP knoc作者: fodlder 時間: 2025-3-26 15:53 作者: 你不公正 時間: 2025-3-26 17:52
Loss of Cone and Reduction in Rod ERG Responses in the Guanylyl Cyclase-E (GC-E) Deficient Mousehomolog of the rodent GC-E gene have been reported in patients with Leber congenital amaurosis (LCA) and in patients with cone-rod dystrophy (CORD6). We have recently produced a mouse genetic model lacking the GC-E gene, and have recorded electroretinograms (ERGs) from mice at different ages. Rod ER作者: 心痛 時間: 2025-3-26 22:46
Guanylyl Cyclase Gene is the Disease Locus in the , Chickenled electrophysiological, morphological, and biochemical analyses of the retinas of these animals, the results of which provided a comprehensive description of the pathology of this retinal degenerative disease, and the first clues concerning the identity of the . gene. In 1990, we embarked on a ser作者: 記成螞蟻 時間: 2025-3-27 04:26 作者: Disk199 時間: 2025-3-27 06:07 作者: 墊子 時間: 2025-3-27 11:15
Rhodopsin C-Terminal Sequence Qvs(A)Pa Directs Its Sorting To The Ros In Retinal Photoreceptorsies have implicated the C-terminal domain of rhodopsin in its trafficking on specialized post-Golgi membranes to the rod outer segment (ROS) of the photoreceptor cell. In addition, aberrant subcellular localization of rhodopsin has been observed in transgenic animals carrying C-terminal mutations. T作者: 異端邪說2 時間: 2025-3-27 13:59 作者: 巡回 時間: 2025-3-27 21:09
A Homozygous 1-Base Pair Deletion (1147dela) in the Arrestin Gene in Autosomal Recessive Retinitis Pt one in 3000 to 10,000 people in many countries, and it is a leading cause of blindness in the adult population. Several kinds of mutations have been reported in patients with autosomal recessive RP (arRP) in genes that are normally expressed in rod photoreceptors and that function in the process o作者: dysphagia 時間: 2025-3-28 01:21
mRNA Analysis of Oguchi Patients with the Frequent 1147delA Mutation in the Arrestin Genen in the arrestin gene causes Oguchi disease and autosomal recessive retinitis pigmentosa in Japanese patients. We examined expression of arrestin in mRNA isolated from whole blood cells of patients with Oguchi disease, who had the 1147delA mutation in the arrestin gene. Arrestin was expressed at th作者: CAMEO 時間: 2025-3-28 02:16
Mutation Spectrum in the , Gene of Japanese Choroideremia Patientst our previous case report. We performed multi-institutional study of the . gene in Japanese patients with choroideremia...: Twenty four unrelated Japanese families with choroideremia were analyzed. It included 24 patients and a carrier. The method for screening was a nonradioisotopic modification o作者: TIGER 時間: 2025-3-28 08:45
Phenotype-Genotype Correlations in Retinal Degenerations Caused by Abcr gene Mutationsnd adulthood, respectively. Recently, mutations of the photoreceptor cell-specific ATP binding transporter gene (ABCR) have been reported in STGD on one hand, and in some age related macular dystrophies (AMD) on the other hand. In addition, autosomal recessive retinitis pigmentosa (RP19) has recentl作者: 材料等 時間: 2025-3-28 14:21 作者: 逢迎春日 時間: 2025-3-28 16:57 作者: VOK 時間: 2025-3-28 19:50
CRALBP and Inherited Retinal Degenerationblishing that the arRP modification was responsible for a loss of protein function. In addition, we present progress in the development of CRALBP knockout mice for studying . functions and therapeutic approaches to retinal degenerations related to CRALBP.作者: antipsychotic 時間: 2025-3-29 01:47
Autosomal Dominant Macular Degeneration Localized to Chromosome 6q by Linkage Analysisterval on chromosome 6q11–13 and excludes the loci for North Carolina Macular Dystrophy and Progressive Bifocal Chorioretinal Atrophy. Three other retinalJ.macular dystrophies map to overlapping intervals and could be allelic forms of the same gene or from a cluster of genes causing retinal/macular degeneration.作者: Perineum 時間: 2025-3-29 05:36
um on Retinal Degeneration as a satellite meeting of the International Congress of Eye Research. The timing and varying location of these meetings provides an important assembly for investigators from throughout the world to convene for presentation of their new findings on the causes and potential 作者: exorbitant 時間: 2025-3-29 08:02 作者: Chandelier 時間: 2025-3-29 13:15 作者: critique 時間: 2025-3-29 15:48
Loss of Cone and Reduction in Rod ERG Responses in the Guanylyl Cyclase-E (GC-E) Deficient Mouseable cone ERG in mice >8 wks. An early loss of cones or a failure of cones to develop was confirmed by histological analysis. The maximum rod photoresponse amplitude (.) was 70% lower than normal at 3–5 wks despite a normal histological appearance of rods. Recovery from activation, as assessed by a 作者: 芳香一點 時間: 2025-3-29 22:00
Leber’s Congenital Amaurosisetinal findings appeared. None of the 9 reexamined patients showed a normal fundus. Nystagmus and strabismus were principal presenting symptoms. Eleven patients presented with the oculodigital sign, three of them were enophthalmic, and 12 patients showed roving eye movements. Patients with additiona作者: 施加 時間: 2025-3-30 03:10 作者: SMART 時間: 2025-3-30 07:10 作者: hurricane 時間: 2025-3-30 09:34
The Cytoplasmic Tail of Rhodopsin Acts as a Sorting Signal in Polarized Photoreceptors and MDCK Cellll body to the rod outer segment, where phototransduction occurs. Several mutant rhodopsins, found in patients with autosomal dominant retinitis pigmentosa (ADRP), have an amino acid change at the carboxy-terminus and these mutants are defective in their outer segment localization. It will be of int作者: Spinal-Fusion 時間: 2025-3-30 16:01 作者: CONE 時間: 2025-3-30 20:30
Mutation Spectrum in the , Gene of Japanese Choroideremia Patients background different from families reported before confirm that the . gene defect causes choroideremia. Most of Japanese patients with choroideremia are caused by the . gene mutations. No missense mutation has been found in Japanese patients either. Although large deletion was sometimes recognized 作者: 亞麻制品 時間: 2025-3-30 23:08 作者: Instantaneous 時間: 2025-3-31 04:32
Book 1999proceedings volume, reflects a strong emphasis on the molecular genetic approach to understa- ing these disorders. Several of the papers provide important new insights into the mechanism of photoreceptor degeneration and cell death. A number of the studies are targeted at retarding or reversing the 作者: 一窩小鳥 時間: 2025-3-31 08:43
d in this proceedings volume, reflects a strong emphasis on the molecular genetic approach to understa- ing these disorders. Several of the papers provide important new insights into the mechanism of photoreceptor degeneration and cell death. A number of the studies are targeted at retarding or reversing the 978-1-4757-7224-1978-0-585-33172-0作者: 絕食 時間: 2025-3-31 10:15
David S. Williams,Xinran Liu,Gordon Vansant,Brian Ondekgional research networks for global change science in developing countries, stimulates and carries out global change research in developing regions of the world, and builds capacity to undertake such research a978-3-642-62693-7978-3-642-56228-0Series ISSN 1619-2435 作者: extrovert 時間: 2025-3-31 15:04 作者: Venules 時間: 2025-3-31 18:20 作者: Consequence 時間: 2025-3-31 22:00
Jean-Michel Rozet,Sylvie Gerber,Imad Ghazi,Isabelle Perrault,Eric Souied,Dominique Ducroq,Annick Cab作者: Favorable 時間: 2025-4-1 03:56 作者: 投射 時間: 2025-4-1 08:31
Retinal Degenerative Diseases and Experimental Therapy作者: 刀鋒 時間: 2025-4-1 12:19
Joe G. Hollyfield,Robert E. Anderson,Matthew M. La作者: 固定某物 時間: 2025-4-1 15:20
