作者: 復(fù)習(xí) 時間: 2025-3-21 21:51 作者: Gesture 時間: 2025-3-22 01:35 作者: 冷淡周邊 時間: 2025-3-22 05:11
Jillian P. Casey,Ellen Crushell,Kyle Thompson,Eilish Twomey,Langping He,Sean Ennis,Roy K. Philip,Robes of results that end-users expect, the optimisation requirements of this approach are considered. Finally, the particular types of problems which agricultural systems models pose are listed and discussed. Practical methods of dealing with these problems are outlined, again using agricultural examp作者: Obverse 時間: 2025-3-22 11:59
S. Schulte Althoff,M. Grüneberg,J. Reunert,J. H. Park,S. Rust,C. Mühlhausen,Y. Wada,R. Santer,T. Marhe plaintext (message) is encrypted using chaotic signals at the drive system side. The resulting ciphertext is embedded to the output and/or state of the drive system and is sent via public channel to the response system. The plaintext is retrieved via the synthesis approach, i.e. the designed unkn作者: 解開 時間: 2025-3-22 16:26
Ehud Banne,Vardiella Meiner,Avraham Shaag,Rachel Katz-Brull,Ayelet Gamliel,Stanley Korman,Smadar Horhe parameters of selected evolutionary algorithms. Investigation consists of four different case studies with increasing simulation complexity. For all algorithms each simulation was evaluated 100 times in order to show and check robustness of used methods. All data were processed and used in order 作者: Laconic 時間: 2025-3-22 18:07 作者: 認(rèn)為 時間: 2025-3-22 23:05 作者: 箴言 時間: 2025-3-23 03:31 作者: SPALL 時間: 2025-3-23 06:08
Katalin M. Ross,Laurie M. Brown,Michelle M. Corrado,Tayoot Chengsupanimit,Latravia M. Curry,Iris A. om leading international researchers provide the reader with a variety of perspectives, including a special focus on the combination of EAs with problem specific heuristics...Evolutionary Algorithms for Embedded System Design. is an excellent reference for both practitioners working in the area of c作者: Entropion 時間: 2025-3-23 11:20 作者: Pcos971 時間: 2025-3-23 14:16
Thabata Caroline da Rocha Siqueira,Carolina Fischinger Moura de Souza,Paulo Lompa,Mercedes Picarellilife, adaptive behavior, artificial immune systems, agent-based systems, neural computing, fuzzy systems, and quantum computing as long as GEC techniques are part of or inspiration for the system being described. This encyclopedic volume on the use of the algorithms of genetic and evolu- tionary com作者: 規(guī)范要多 時間: 2025-3-23 21:15 作者: FANG 時間: 2025-3-23 22:36 作者: 發(fā)怨言 時間: 2025-3-24 02:21 作者: 敲詐 時間: 2025-3-24 06:51 作者: refine 時間: 2025-3-24 13:47 作者: cataract 時間: 2025-3-24 15:58 作者: 縱欲 時間: 2025-3-24 19:20
Energy Expenditure in Chilean Children with Maple Syrup Urine Disease (MSUD),ture variables, there was no significant difference between groups. Moreover, compared to BEEr, equations underestimate according to BEE WHO and Schofield, respectively (.?=?0.00; 0.02). The WHO equation had lower average calorie difference, greater concordance correlation and association with indir作者: 不幸的人 時間: 2025-3-25 02:57 作者: senile-dementia 時間: 2025-3-25 03:31
Safety and Efficacy of Chronic Extended Release Cornstarch Therapy for Glycogen Storage Disease Typ in 82 patients (88%) with GSD Ia and 10 patients (77%) with GSD Ib. The success rate for extending fasting was 95% for females and 78% for males. Of the patients who entered the longitudinal phase, long-term data are available for 44 subjects. Mean duration of fasting on traditional cornstarch prio作者: 清真寺 時間: 2025-3-25 10:50
Normal Neurodevelopmental Outcomes in PNPO Deficiency: A Case Series and Literature Review,dase deficiency and electively treating with pyridoxal-5′-phosphate is considered in any neonate with encephalopathy, including those with presumed hypoxic ischemic encephalopathy in whom the degree of encephalopathy is not expected from perinatal history, cord gases and/or neuroimaging.作者: Genetics 時間: 2025-3-25 12:53
Screening for Attenuated Forms of Mucopolysaccharidoses in Patients with Osteoarticular Problems ofedic services in Porto Alegre, Brazil. The screened patients presented with articular manifestations with no defined etiology. These patients were screened by quantitative and qualitative assessment of urinary GAGs...: Among the 55 cases investigated, one 15-year-old patient exhibited increased urin作者: dysphagia 時間: 2025-3-25 18:08 作者: geometrician 時間: 2025-3-25 22:42
A. Ahmed,K. Rudser,A. Kunin-Batson,K. Delaney,C. Whitley,E. Shapiroediction problems. It provides a tutorial on how to design, adapt, and evaluate artificial neural networks as well, and includes source codes for most of the proposed techniques as supplementary materials..978-3-030-06572-0978-3-319-93025-1Series ISSN 1860-949X Series E-ISSN 1860-9503 作者: 食料 時間: 2025-3-26 03:33
Karen Campo,Gabriela Castro,Valerie Hamilton,Juan Francisco Cabello,Erna Raimann,Carolina Arias,Veróediction problems. It provides a tutorial on how to design, adapt, and evaluate artificial neural networks as well, and includes source codes for most of the proposed techniques as supplementary materials..978-3-030-06572-0978-3-319-93025-1Series ISSN 1860-949X Series E-ISSN 1860-9503 作者: consent 時間: 2025-3-26 07:01
Esther Schrapers,Laura C. Tegtmeyer,Gunter Simic-Schleicher,Volker Debus,Janine Reunert,Sebastian Baediction problems. It provides a tutorial on how to design, adapt, and evaluate artificial neural networks as well, and includes source codes for most of the proposed techniques as supplementary materials..978-3-030-06572-0978-3-319-93025-1Series ISSN 1860-949X Series E-ISSN 1860-9503 作者: hemorrhage 時間: 2025-3-26 08:47 作者: 極大的痛苦 時間: 2025-3-26 12:52 作者: reperfusion 時間: 2025-3-26 19:32
Book 2016JIMD Reports publishes case and short researchreports in the area of inherited metabolic disorders. Case reports highlightsome unusual or previously unrecorded feature relevant to the disorder, orserve as an important reminder of clinical or biochemical features of aMendelian disorder.作者: 并入 時間: 2025-3-26 21:11
https://doi.org/10.1007/978-3-662-49833-0inherited metabolic diseases; pediatrics; medical genetics; Mendelian disorder; endocrinology; metabolic 作者: OTHER 時間: 2025-3-27 03:52 作者: 用手捏 時間: 2025-3-27 06:42
JIMD Reports, Volume 26978-3-662-49833-0Series ISSN 2192-8304 Series E-ISSN 2192-8312 作者: Type-1-Diabetes 時間: 2025-3-27 09:50
Friedreich Ataxia in Classical Galactosaemia,stence of classical galactosaemia and Friedreich ataxia (FRDA) in nine children from seven Irish Traveller families. These two autosomal recessive disorders, the loci for which are located on either side of the centromere of chromosome 9, appear to be in linkage disequilibrium in this subgroup. Both作者: modifier 時間: 2025-3-27 13:46
Phenotypic Expansion of Congenital Disorder of Glycosylation Due to , Null Mutation,disability, seizures with hypsarrhythmia (West syndrome), hepatosplenomegaly, increased serum transaminases, iris coloboma, glaucoma, corneal clouding and bilateral dilated lateral ventricles, and extra-axial post-cerebellar space. Serum transferrin isoelectrofocusing (IEF) showed a type 1 pattern. 作者: 泄露 時間: 2025-3-27 20:05 作者: 使人煩燥 時間: 2025-3-28 01:36
TMEM165 Deficiency: Postnatal Changes in Glycosylation,anism, a mutation in a single gene leads to a multisystemic disorder. We describe a patient with TMEM165-CDG with facial dysmorphism, nephrotic syndrome, cardiac defects, enlarged cerebral ventricles, feeding problems, and neurological involvement. Having confirmed the diagnosis via prenatal diagnos作者: 險代理人 時間: 2025-3-28 05:56
Transaldolase Deficiency: A New Case Expands the Phenotypic Spectrum,smorphic features. We report a case presenting prenatally with hyperechogenic bowel and intrauterine growth restriction. The infant was born small for gestational age, with cutis laxa and hypertrichosis. Postnatally, meconium plug was identified, complicated with intestinal obstruction necessitating作者: 聾子 時間: 2025-3-28 06:49
Pearson Syndrome: A Retrospective Cohort Study from the Marrow Failure Study Group of A.I.E.O.P. (A central nervous system. It is characterized principally by a transfusion-dependent anemia that usually improves over time, a tendency to develop severe infections, and a high mortality rate. We describe a group of 11 PS patients diagnosed in Italy in the period 1993–2014. The analysis of this reaso作者: prick-test 時間: 2025-3-28 10:42
Bioimpedance Analysis as a Method to Evaluate the Proportion of Fatty and Muscle Tissues in Progrese to body mass provides an indication of the extent of muscle tissue destruction, i.e., the progression and severity of the disease..In this study we use Pompe disease as an example to report the new possibility of using bioimpedance analysis (BIA) to assess the relative proportion of fatty and musc作者: JECT 時間: 2025-3-28 17:58
Infantile Refsum Disease: Influence of Dietary Treatment on Plasma Phytanic Acid Levels, from a generalized peroxisomal function impairment. Increased plasma levels of very long chain fatty acids (VLCFA) and phytanic acid are biomarkers used in IRD diagnosis. Furthermore, an increased plasma level of phytanic acid is known to be associated with neurologic damage. Treatment of IRD is sy作者: Externalize 時間: 2025-3-28 21:33
Mucopolysaccharidosis (MPS) Physical Symptom Score: Development, Reliability, and Validity,polysaccharidoses (MPS) to track disease and monitor treatments. We examined scoring reliability, its concurrent validity with other measures, and relationship to age in MPS type I...: Fifty-four patients with MPS I (36 with Hurler syndrome treated with hematopoietic cell transplant and 18 with atte作者: 有常識 時間: 2025-3-29 01:06 作者: 入會 時間: 2025-3-29 05:10
News on Clinical Details and Treatment in PGM1-CDG, disorders of glycosylation (CDG) and glycogen storage diseases..This paper focuses on previously reported siblings with short stature, hypothyroidism, increased transaminases, and, in one of them, dilated cardiomyopathy (DCM). An intronic point mutation in the PGM1-gene (c.1145-222 G>T) leads to a 作者: 把…比做 時間: 2025-3-29 08:19 作者: 做方舟 時間: 2025-3-29 12:57 作者: 清晰 時間: 2025-3-29 17:16
Screening for Attenuated Forms of Mucopolysaccharidoses in Patients with Osteoarticular Problems ofS are multisystemic conditions that affect the entire body, with variations in the clinical presentation, having specific treatments available depending on the type of MPS. Nearly all MPS disorders compromise the osteoarticular system in different ways, and virtually all patients have abnormal urina作者: 膽小鬼 時間: 2025-3-29 20:18
Causes of Death in Adults with Mitochondrial Disease,sease progression. It might therefore be expected that this variation be reflected in the age and cause of death. However, to date, little has been reported regarding the ‘end-of-life’ period and causes of death in mitochondrial disease patients. For some specific syndromes, the associated clinical 作者: 發(fā)牢騷 時間: 2025-3-30 02:02
gorithms.A new empirical tool for comparing search and optimDespite decades of work in evolutionary algorithms, there remains a lot of uncertainty as to when it is beneficial or detrimental to use recombination or mutation. This book provides a characterization of the roles that recombination and mu作者: Neuropeptides 時間: 2025-3-30 08:05 作者: nauseate 時間: 2025-3-30 09:30 作者: Ergots 時間: 2025-3-30 12:33
