作者: Isolate 時間: 2025-3-21 23:59 作者: 杠桿 時間: 2025-3-22 04:13 作者: 大方一點 時間: 2025-3-22 05:36
Infantile Hypophosphatasia Secondary to a Novel Compound Heterozygous Mutation Presenting with Pyri作者: 指令 時間: 2025-3-22 09:24 作者: Pruritus 時間: 2025-3-22 15:06
Motor and Speech Disorders in Classic Galactosemia,作者: 礦石 時間: 2025-3-22 17:46 作者: 合群 時間: 2025-3-23 00:57
Cerebral Magnetic Resonance Spectroscopy Demonstrates Long-Term Effect of Bone Marrow Transplantati作者: 儲備 時間: 2025-3-23 04:30
,Early Cardiac Changes in Children with Anderson–Fabry Disease,作者: 窩轉(zhuǎn)脊椎動物 時間: 2025-3-23 07:07
Development of a Scoring System to Evaluate the Severity of Craniocervical Spinal Cord Compression 作者: 不足的東西 時間: 2025-3-23 11:52
Outcome of Perinatal Hypophosphatasia in Manitoba Mennonites: A Retrospective Cohort Analysis,作者: arbiter 時間: 2025-3-23 17:47
Novel Deletion Mutation Identified in a Patient with Late-Onset Combined Methylmalonic Acidemia and作者: kidney 時間: 2025-3-23 19:08
Substrate Reduction Therapy in Four Patients with Milder , Mutations and Juvenile-Onset Batten Dise作者: Dna262 時間: 2025-3-23 22:28
,A Clinically Severe Variant of β-Mannosidosis, Presenting with Neonatal Onset Epilepsy with Subsequ作者: Largess 時間: 2025-3-24 03:47
A Novel Exonic Splicing Mutation in the , (,) Gene in a Case with Atypical Barth Syndrome,作者: uveitis 時間: 2025-3-24 09:53 作者: extract 時間: 2025-3-24 11:59
Mitochondrial Infantile Liver Disease due to , Gene Mutations: Three New Cases,作者: 細頸瓶 時間: 2025-3-24 16:14
,Spondyloepiphyseal Dysplasias and Bilateral Legg-Calvé-Perthes Disease: Diagnostic Considerations f作者: 四牛在彎曲 時間: 2025-3-24 20:47 作者: Hypopnea 時間: 2025-3-24 23:23
Else R. Danielsen,Allan M. Lund,Carsten Thomsen versions of the papers delivered in Washington. This has allowed greater coverage of the topics in question. I suggested a format of a general overview of a to978-1-4615-6943-5978-1-4615-6941-1Series ISSN 0172-6625 作者: gene-therapy 時間: 2025-3-25 05:09
ocollaborate. Their inputs have been intensively discussed ina workshop. The book is the output of the workshop. Thefirst goal of the bookis to give the reader an insight intobasic principles about the evolutionof informationprocessing systems. This, however, leads directly to a veryold and essential question978-3-642-77213-9978-3-642-77211-5作者: Basal-Ganglia 時間: 2025-3-25 10:20
Filippo Vairo,Cristina Netto,Alicia Dorneles,Suzana Mittelstadt,Matheus Wilke,Divair Doneda,Kristianation for learning something new, may induce stress related disorders. Similarly, expecting a more competent individual to undergo numerous simple test-items can generate the same negative result. A Competency Management System (CMS) is presented to initiate effective human-computer interaction (HCI作者: Increment 時間: 2025-3-25 14:26 作者: Largess 時間: 2025-3-25 19:46
Claire Searle,Brage Storstein Andresen,Ed Wraith,Jamie Higgs,Deborah Gray,Alison Mills,K. Elizabeth users to generate breakthrough innovations with a revenue potential eight times higher than that of ideas from conventional ideation approaches (von Hippel et al. 1999). The foundations of this phenomenon have been laid by von Hippel’s seminal work on the . in the late 1970s (von Hippel 1978) and o作者: indoctrinate 時間: 2025-3-25 21:27
Dina Belachew,Traci Kazmerski,Ingrid Libman,Amy C. Goldstein,Susan T. Stevens,Stephanie DeWard,Jerryre developments is poor. The next big thing has been regularly out of sight — not only regarding technological topics like ATM, ISDN, 3G, but especially for usability and user-driven developments like the World Wide Web, SMS, and Web 2.0. Oftentimes outdated mindsets and tunnel vision when imagining作者: 強行引入 時間: 2025-3-26 02:55
E. Santos Silva,M. L. Cardoso,L. Vilarinho,M. Medina,C. Barbot,E. Martins to its control was often suggested by earlier workers. In his work on insect migration, Johnson (1969) put forth a model in which adult migration was triggered when ecdysone was absent and the juvenile hormone (JH) titer was low. The rise in JH titer then caused both the cessation of migratory beha作者: 有效 時間: 2025-3-26 04:59 作者: 模范 時間: 2025-3-26 10:16
Sheetal Sharda,Suresh Kumar Angurana,Mandeep Walia,Savita Attri to its control was often suggested by earlier workers. In his work on insect migration, Johnson (1969) put forth a model in which adult migration was triggered when ecdysone was absent and the juvenile hormone (JH) titer was low. The rise in JH titer then caused both the cessation of migratory beha作者: osculate 時間: 2025-3-26 14:23
Stepan Havranek,Ales Linhart,Zuzana Urbanova,Uma Ramaswamidy of evolutionary problems. In that I think we have succeeded reasonably well. These papers are expanded and in some cases somewhat altered versions of the papers delivered in Washington. This has allowed greater coverage of the topics in question. I suggested a format of a general overview of a to作者: 關(guān)節(jié)炎 時間: 2025-3-26 18:13 作者: 充氣女 時間: 2025-3-27 00:09 作者: 商議 時間: 2025-3-27 04:00
Paul Hoff Backe,Mari Ytre-Arne,?smund Kjendseth R?hr,Else Brodtkorb,Brian Fowler,Helge Rootwelt,MagnThe major firms also encounter greater risks in high-tech sectors, like, for example, Olivetti, while they have a greater life expectancy in the mature low-tech sectors..A third interesting characteristic is the fact that, in the Italian system of firms, there are no small and medium size firms in m作者: 山頂可休息 時間: 2025-3-27 06:55 作者: ciliary-body 時間: 2025-3-27 12:38
A Broomfield,R Gunny,I Ali,A Vellodi,P PrabhakarThe major firms also encounter greater risks in high-tech sectors, like, for example, Olivetti, while they have a greater life expectancy in the mature low-tech sectors..A third interesting characteristic is the fact that, in the Italian system of firms, there are no small and medium size firms in m作者: 退潮 時間: 2025-3-27 14:52
Yuxin Fan,Jon Steller,Iris L. Gonzalez,Wim Kulik,Michelle Fox,Richard Chang,Brandy A. Westerfield,AnThe major firms also encounter greater risks in high-tech sectors, like, for example, Olivetti, while they have a greater life expectancy in the mature low-tech sectors..A third interesting characteristic is the fact that, in the Italian system of firms, there are no small and medium size firms in m作者: Ordeal 時間: 2025-3-27 18:56
Alfredo Uribe,Roberto GiuglianiThe major firms also encounter greater risks in high-tech sectors, like, for example, Olivetti, while they have a greater life expectancy in the mature low-tech sectors..A third interesting characteristic is the fact that, in the Italian system of firms, there are no small and medium size firms in m作者: expansive 時間: 2025-3-27 23:06 作者: 小爭吵 時間: 2025-3-28 05:10
Nancy J. Mendelsohn,Timothy Wood,Rebecca A. Olson,Renee Temme,Susan Hale,Haoyue Zhang,Lisa Read,KlanThe major firms also encounter greater risks in high-tech sectors, like, for example, Olivetti, while they have a greater life expectancy in the mature low-tech sectors..A third interesting characteristic is the fact that, in the Italian system of firms, there are no small and medium size firms in m作者: nepotism 時間: 2025-3-28 07:40
R. Parini,F. Furlan,A. Brambilla,D. Codazzi,S. Vedovati,C. Corbetta,T. Fedeli,B. Merinero,B. Pérez,M1978), and Krause (1982) on mammals. Similarly, the present study is based on fossils in order to understand the mechanics of jaw motion in the diverse Mesozoic herbivores known as ornithopods. Most commonly, particularly in work on mammals, vertebrate jaw mechanisms are modeled as class III levers.作者: Eclampsia 時間: 2025-3-28 10:39 作者: Asparagus 時間: 2025-3-28 17:18
JIMD Reportshttp://image.papertrans.cn/j/image/500049.jpg作者: overshadow 時間: 2025-3-28 18:54
Book 2013JIMD Reports publishes case and short research reports in the area of inherited metabolic disorders. Case reports highlight some unusual or previously unrecorded feature relevant to the disorder, or serve as an important reminder of clinical or biochemical features of a Mendelian disorder.作者: FOLLY 時間: 2025-3-28 23:23
https://doi.org/10.1007/978-3-642-37328-2endocrinology; inherited metabolic diseases; medical genetics; pediatrics; metabolic disease作者: 仇恨 時間: 2025-3-29 03:31
978-3-642-37327-5SSIEM and Springer-Verlag Berlin Heidelberg 2013作者: Canary 時間: 2025-3-29 09:26 作者: 結(jié)合 時間: 2025-3-29 12:54
essing. Since thesestructures have been evolved over the last five billionyears, information processing and its systems have anevolution.This is under consideration in the book. Startingwith a basic paper whichsummarizes the essential hypothesesabout the evolution of informaion processing systems,si作者: 使乳化 時間: 2025-3-29 18:56 作者: LITHE 時間: 2025-3-29 23:31
Lance Harrington Rodan,Navin Mishra,Ivanna Yau,Andrea Andrade,Komudi Siriwardena,Ingrid Teinng. When dealing with young adults at different cognitive skill levels, it is important to be able to identify and distinguish between their knowledge/competency levels, mostly on the basis of the evidence gathered from test-items. The current absence of appropriate measurement tools to determine sk作者: 雪白 時間: 2025-3-30 00:08
Claire Searle,Brage Storstein Andresen,Ed Wraith,Jamie Higgs,Deborah Gray,Alison Mills,K. Elizabeth awecki et al. 2010). The instrument involving users from outside the company in ideation is called an . The BMW Group’s idea contests are just one example of a plethora of similar initiatives recently taken by leading innovative companies. Since the turn of the millennium, many companies such as 3M 作者: 河潭 時間: 2025-3-30 07:12
Dina Belachew,Traci Kazmerski,Ingrid Libman,Amy C. Goldstein,Susan T. Stevens,Stephanie DeWard,Jerryith mid- and long-term investments in particular, insufficient information and persistence in mindsets can lead to fundamental threats. Like other high-investment infrastructure companies, telecommunications providers work on 5- to 10-year plans in major parts of their business. Long investment life作者: Minatory 時間: 2025-3-30 11:27
E. Santos Silva,M. L. Cardoso,L. Vilarinho,M. Medina,C. Barbot,E. Martinsare generally extremely responsive to stimuli which induce flight and less responsive or unresponsive to stimuli associated with reproduction and feeding (Kennedy, 1961). In many species migration occurs in response to short photoperiods and is an alternative to immediate reproduction. Often associa作者: 任意 時間: 2025-3-30 13:16
Nancy L. Potter,Yves Nievergelt,Lawrence D. Shribergare generally extremely responsive to stimuli which induce flight and less responsive or unresponsive to stimuli associated with reproduction and feeding (Kennedy, 1961). In many species migration occurs in response to short photoperiods and is an alternative to immediate reproduction. Often associa作者: Ebct207 時間: 2025-3-30 17:40
Sheetal Sharda,Suresh Kumar Angurana,Mandeep Walia,Savita Attriare generally extremely responsive to stimuli which induce flight and less responsive or unresponsive to stimuli associated with reproduction and feeding (Kennedy, 1961). In many species migration occurs in response to short photoperiods and is an alternative to immediate reproduction. Often associa作者: BILE 時間: 2025-3-30 22:51
Else R. Danielsen,Allan M. Lund,Carsten Thomsenogy in Washington, D. C., USA in August, 1976. The choice of topic was prompted by recent advances in evolutionary ecology and the apparent suitability of insect migration and dia- pause as appropriate material for evolutionary studies. In the event, that choice seems amply justified as I hope a per作者: auxiliary 時間: 2025-3-31 01:36
Stepan Havranek,Ales Linhart,Zuzana Urbanova,Uma Ramaswamihington, D. C., USA in August, 1976. The choice of topic was prompted by recent advances in evolutionary ecology and the apparent suitability of insect migration and dia- pause as appropriate material for evolutionary studies. In the event, that choice seems amply justified as I hope a perusal of th作者: 柔軟 時間: 2025-3-31 06:10 作者: 本土 時間: 2025-3-31 11:50 作者: burnish 時間: 2025-3-31 16:04
Paul Hoff Backe,Mari Ytre-Arne,?smund Kjendseth R?hr,Else Brodtkorb,Brian Fowler,Helge Rootwelt,Magn major firms shows a convergence towards the bottom of the size distribution, i.e. these firms grow but, the absolute size does not grow much because the firms that reach the highest stages recede. In fact, the entire universe of firms shows an extended series of ., namely of firms that in the diffe作者: 放肆的你 時間: 2025-3-31 20:14 作者: eucalyptus 時間: 2025-3-31 21:41
A Broomfield,R Gunny,I Ali,A Vellodi,P Prabhakar major firms shows a convergence towards the bottom of the size distribution, i.e. these firms grow but, the absolute size does not grow much because the firms that reach the highest stages recede. In fact, the entire universe of firms shows an extended series of ., namely of firms that in the diffe作者: Metastasis 時間: 2025-4-1 05:37 作者: 禮節(jié) 時間: 2025-4-1 06:19
Alfredo Uribe,Roberto Giugliani major firms shows a convergence towards the bottom of the size distribution, i.e. these firms grow but, the absolute size does not grow much because the firms that reach the highest stages recede. In fact, the entire universe of firms shows an extended series of ., namely of firms that in the diffe作者: N斯巴達人 時間: 2025-4-1 13:49 作者: 官僚統(tǒng)治 時間: 2025-4-1 14:29
