標(biāo)題: Titlebook: Alagille Syndrome; Pathogenesis and Cli Binita M. Kamath,Kathleen M. Loomes Book 2018 Springer International Publishing AG, part of Springe [打印本頁(yè)] 作者: 從未沮喪 時(shí)間: 2025-3-21 18:04
書目名稱Alagille Syndrome影響因子(影響力)
書目名稱Alagille Syndrome影響因子(影響力)學(xué)科排名
書目名稱Alagille Syndrome網(wǎng)絡(luò)公開度
書目名稱Alagille Syndrome網(wǎng)絡(luò)公開度學(xué)科排名
書目名稱Alagille Syndrome被引頻次
書目名稱Alagille Syndrome被引頻次學(xué)科排名
書目名稱Alagille Syndrome年度引用
書目名稱Alagille Syndrome年度引用學(xué)科排名
書目名稱Alagille Syndrome讀者反饋
書目名稱Alagille Syndrome讀者反饋學(xué)科排名
作者: Anemia 時(shí)間: 2025-3-21 23:26 作者: 種類 時(shí)間: 2025-3-22 02:28 作者: output 時(shí)間: 2025-3-22 04:43
Transplant Considerations in Alagille Syndrome,tage liver disease. It is a well-established therapy with reasonable success. The multi-system nature of this condition dictates a considered approach to liver transplant evaluation and management in order to assure a good outcome.作者: FIN 時(shí)間: 2025-3-22 12:18
Binita M. Kamath,Kathleen M. LoomesProvides a concise yet comprehensive overview of Alagille syndrome.Outlines management challenges, strategies, and future treatment options.Written by experts in the field作者: mortuary 時(shí)間: 2025-3-22 15:29 作者: 規(guī)范要多 時(shí)間: 2025-3-22 17:38 作者: tenuous 時(shí)間: 2025-3-22 22:17
Discrete Time: Smoothing Algorithms,icate, arborizing, hierarchical network of ducts that navigate the liver parenchyma, contributing to liver health and disease not only via drainage of bile but via direct and indirect interactions with surrounding cells. Development of the intrahepatic bile ducts depends upon cell specification and 作者: 使厭惡 時(shí)間: 2025-3-23 03:12 作者: Trochlea 時(shí)間: 2025-3-23 07:16 作者: Mnemonics 時(shí)間: 2025-3-23 12:55 作者: GLIDE 時(shí)間: 2025-3-23 15:56
https://doi.org/10.1007/978-3-540-74703-1es, the most common cardiovascular abnormality, is one of the five elements used in the clinical diagnosis of this syndrome. Other commonly occurring lesions include tetralogy of Fallot, pulmonary valve stenosis or atresia, valvar or supravalvar aortic stenosis, and aortic coarctation. The periphera作者: Hippocampus 時(shí)間: 2025-3-23 21:47 作者: 協(xié)迫 時(shí)間: 2025-3-23 23:44
Jean-No?l Thépaut,Erik Andersson Notch signaling pathway as a consequence of . and . mutations result in the diverse manifestations of ALGS. Notch signaling plays a central role in the development of multiple tissues and organs but particularly of the kidneys. Understanding the role of Notch signaling in renal development helps in作者: watertight, 時(shí)間: 2025-3-24 02:31 作者: facetious 時(shí)間: 2025-3-24 07:50 作者: 高爾夫 時(shí)間: 2025-3-24 13:29 作者: Gene408 時(shí)間: 2025-3-24 16:05
Peiming Dong,Ke Zhong,Sixiong Zhao ensuring nutrition and managing symptoms such as pruritus and in some cases liver and/or heart transplantation. In this chapter, future potential therapies or cures for Alagille syndrome are discussed, as well as state-of-the-art systems for drug discovery..Future potential strategies range from tr作者: 使虛弱 時(shí)間: 2025-3-24 19:39
Jean-No?l Thépaut,Erik Anderssonthway plays a role in the evolution of chronic renal injury. How that response to renal injury is altered in ALGS and its impact on the clinical sequelae in ALGS is not known. Given the frequency of renal findings in ALGS, kidney specialists should form part of the multidisciplinary care team for these patients.作者: Glutinous 時(shí)間: 2025-3-25 02:40
Fully Nonlinear Data AssimilationALGS having had recurrent infections have been described with an immune profile compatible with a persistent pro-inflammatory immune state related to failure of the Jagged1-Notch-CD46 system. Studies to elucidate the prevalence, cohort clinical significance, and optimal management have still to be undertaken.作者: 迅速成長(zhǎng) 時(shí)間: 2025-3-25 03:21
,The Renal Sequelae of Alagille Syndrome as a?Product of Altered Notch Signaling During Kidney Develthway plays a role in the evolution of chronic renal injury. How that response to renal injury is altered in ALGS and its impact on the clinical sequelae in ALGS is not known. Given the frequency of renal findings in ALGS, kidney specialists should form part of the multidisciplinary care team for these patients.作者: Semblance 時(shí)間: 2025-3-25 09:33
,Immune Dysregulation in Alagille Syndrome: A Feature of the?Evolving Phenotype,ALGS having had recurrent infections have been described with an immune profile compatible with a persistent pro-inflammatory immune state related to failure of the Jagged1-Notch-CD46 system. Studies to elucidate the prevalence, cohort clinical significance, and optimal management have still to be undertaken.作者: Esalate 時(shí)間: 2025-3-25 12:18 作者: debouch 時(shí)間: 2025-3-25 16:34 作者: thrombosis 時(shí)間: 2025-3-25 21:54
Assimilation of Operational Databecoming accepted that all patients undergo screening imaging with computed tomography scan or magnetic resonance angiography. This is particularly important in those undergoing liver transplantation or major surgery.作者: stress-test 時(shí)間: 2025-3-26 02:41
,Bile Duct Development and the?Notch Signaling Pathway,re complete insight into the complexities of intrahepatic bile duct development and the signaling pathways involved (Notch and others) is a requisite preamble to defining cellular and molecular therapies with the potential of attenuating, or reversing, biliary injury in Alagille syndrome and other cholangiopathies.作者: itinerary 時(shí)間: 2025-3-26 06:58 作者: gratify 時(shí)間: 2025-3-26 09:14 作者: Petechiae 時(shí)間: 2025-3-26 15:49 作者: Anticoagulant 時(shí)間: 2025-3-26 19:40
Book 2018eatment options..Written by experts in the field,?.Alagille Syndrome: Pathogenesis and Clinical Management.?is a valuable resource for physicians and researchers dealing with this disorder, one that will help guide patient management and stimulate investigative efforts.??.作者: 注視 時(shí)間: 2025-3-26 23:27
https://doi.org/10.1007/978-3-540-74703-1l vasculature is frequently affected as well. In this chapter, we discuss in detail the spectrum and incidence of congenital cardiovascular disease in patients with Alagille syndrome, as well as recommended diagnostic approaches and findings, surveillance, management, and outcomes.作者: 推遲 時(shí)間: 2025-3-27 01:29 作者: ASTER 時(shí)間: 2025-3-27 08:47
Alagille Syndrome: Overview and Introduction,cription, there are many current clinical challenges and opportunities for the development of novel and effective therapies. In the subsequent chapters of this book, the extensive compilation of the knowledge about Alagille syndrome and Notch signaling will serve as a framework for investigation and作者: CAMP 時(shí)間: 2025-3-27 11:41
Genetics of Alagille Syndrome,A hypothesis in the field is that another gene may function to modify features of the disease, and a growing number of candidate gene modifiers have now been proposed. We hope that further understanding of both the variable expressivity of this disease and the molecular function of reported missense作者: 他日關(guān)稅重重 時(shí)間: 2025-3-27 17:24
Liver Disease in Alagille Syndrome,liver disease, cirrhosis, portal hypertension, and eventual need for liver transplantation. There is no specific treatment for hepatic disease in Alagille syndrome, and management focuses on treatment of symptoms of chronic cholestasis, including pruritus, xanthomata, malnutrition, and fat-soluble v作者: 巨碩 時(shí)間: 2025-3-27 17:51 作者: 字謎游戲 時(shí)間: 2025-3-27 23:19
Health-Related Quality of Life and Neurocognition in Alagille Syndrome,evelopment needs should be considered and assessed continuously to improve cognitive outcomes in the ALGS population. Multicenter research networks are needed to study neurocognitive outcomes in this very heterogeneous disease.作者: 舊式步槍 時(shí)間: 2025-3-28 03:41 作者: NAG 時(shí)間: 2025-3-28 09:17 作者: wreathe 時(shí)間: 2025-3-28 11:26 作者: 喃喃而言 時(shí)間: 2025-3-28 15:41 作者: liposuction 時(shí)間: 2025-3-28 21:16 作者: single 時(shí)間: 2025-3-28 23:28 作者: POWER 時(shí)間: 2025-3-29 04:46
Peiming Dong,Ke Zhong,Sixiong Zhao, and our improved understanding of endogenous reparative mechanisms. These putative therapeutic possibilities hold great potential for Alagille syndrome and are also highly translatable to other disease states in which the liver or heart is compromised.作者: 低位的人或事 時(shí)間: 2025-3-29 09:41 作者: COLIC 時(shí)間: 2025-3-29 15:21
,Bile Duct Development and the?Notch Signaling Pathway,icate, arborizing, hierarchical network of ducts that navigate the liver parenchyma, contributing to liver health and disease not only via drainage of bile but via direct and indirect interactions with surrounding cells. Development of the intrahepatic bile ducts depends upon cell specification and 作者: Asymptomatic 時(shí)間: 2025-3-29 16:02 作者: Hemoptysis 時(shí)間: 2025-3-29 20:55
Liver Disease in Alagille Syndrome,commonly presents in the neonatal period during evaluation for cholestasis with elevated bilirubin and GGT. The classic finding on liver biopsy is bile duct paucity; however, this is not diagnostic and not all children with Alagille syndrome have paucity on liver biopsy. There are specific clinical
